European Journal of Cardio-Thoracic Surgery 46 (2014) 921 doi:10.1093/ejcts/ezu052 Advance Access publication 26 February 2014
IMAGES IN CARDIO-THORACIC SURGERY
Unusual complication of neurofibromatosis Andrew Chatzisa,*, Meletios Kanakisa, Achilleas Liouliasb and Fotios Mitropoulosa a b
Department of Paediatric and Congenital Cardiac Surgery, Onassis Cardiac Surgery Centre, Athens, Greece Department of Thoracic Surgery, Sismanogleion General Hospital, Athens, Greece
* Corresponding author. Department of Paediatric and Congenital Cardiac Surgery, Onassis Cardiac Surgery Centre, 356 Syngrou Ave., Kallithea 17674, Athens, Greece. Tel: +30-2109493318; fax: +30-2109493887; e-mail:
[email protected] (A. Chatzis). Received 13 November 2013; received in revised form 28 December 2013; accepted 15 January 2014
Keywords: Neurofibroma • Trachea
A 14-year old boy with neurofibromatosis type I underwent surgery for severe kyphoscoliosis (Fig. 1A). Impaired ventilation led to the termination of the procedure. Investigation revealed
tracheal compression by the innominate artery and a tumour (Fig. 1B–D). The latter was excised via right thoracotomy (Fig. 2). Histology revealed neurofibroma.
Figure 2: (A) Operative view. Tumour (arrowheads); (B) excised tumour; (C) skin neurofibromatosis lesions. I: innominate artery; T: trachea.
IMAGES IN CARDIOTHORACIC SURGERY
Figure 1: (A) Chest X-ray: severe kyphoscoliosis; (B–D): computed tomography scan: trachea compressed between the innominate artery and a tumour, identified after surgery as neurofibroma.
© The Author 2014. Published by Oxford University Press on behalf of the European Association for Cardio-Thoracic Surgery. All rights reserved.