Images in Cardiothoracic Medicine and Surgery
Scimitar syndrome: A rare cause of dyspnea and chest pain
Asian Cardiovascular & Thoracic Annals 2014, Vol. 22(6) 751–752 ß The Author(s) 2013 Reprints and permissions: sagepub.co.uk/journalsPermissions.nav DOI: 10.1177/0218492313489564 aan.sagepub.com
Isa Do¨ngel1, Elif Nisa Unlu2 and Rasih Yazkan1
Figure 1. Axial computed tomography at the level of the right lower lobe, showing (a) drainage of the right main pulmonary vein into the inferior vena cava (short arrow), and (b) the small (hypoplastic) lower lobe of the right lung. (c, d) Coronal maximum intensity projection images clearly show a dilated anomalous vein (right main pulmonary vein) that drains into the inferior vena cava at the level of the lung bases (arrow).
1 Department of Thoracic Surgery, Su¨leyman Demirel University Medical Faculty, Isparta, Turkey 2 Department of Radiology, Su¨leyman Demirel University Medical Faculty, Isparta, Turkey
Corresponding author: Isa Do¨ngel, MD, Department of Thoracic Surgery, Su¨leyman Demirel University Medical Faculty, Isparta, Turkey. Email:
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Asian Cardiovascular & Thoracic Annals 22(6)
Figure 2. (a–d) Volume-rendered reformatted images demonstrating that the anomalous vein drains into the inferior vena cava (venous structures are blue colored and marked with arrows).
A 32-year-old woman presented to our clinic with chest pain and shortness of breath. Physical examination was unremarkable. Pulmonary function tests were: forced expiratory volume in 1 s: 1.96 (79.9%); forced expiratory volume in 1 s/forced vital capacity: 80.64%; forced vital capacity: 2.42 (85.6%); and blood gas values were pH 7.44, pCO2 34.6, pO2 89, HCO3 23.5, sO2 97.3. Pulmonary computed tomographic angiography showed a large right pulmonary vein draining to the inferior vena cava, and hypoplasia of the right lower lobe (Figures 1 and 2). Echocardiography showed an
ejection fraction of 60% and pulmonary artery pressure of 25 mm Hg. The patient has been followed conservatively due to normal oxygenation and cardiac function. Funding This research received no specific grant from any funding agency in the public, commerical, or not-for-profit sectors.
Conflict of interest statement None declared
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